Browsing by Author "Fava, M."

Now showing 1 - 4 of 4
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    Congenital hepatic fibrosis. Report of five cases.
    (2004) Harris, Paul R.; Fodor, D.; Cavagnaro, F.; Di Egidio, M.; Duarte, I.; Fava, M.
    Background. Congenital hepatic fibrosis (CHF) is an autosomic dominant disease that has been associated with polycystic kidney disease. Aim: To describe the medical management of 5 children with CHF and to evaluate the presence and extension of the associated renal disease. Patients and methods: Retrospective review of the medical charts of 5 children with CHF, aged 2 to 14 years. Results: Three children presented autosomic recessive polycystic kidney disease, which was diagnosed before the appearance of liver disease manifestations. They presented a more severe liver damage, with a more aggressive clinical course requiring use of transjugular intrahepatic porto-systemic shunts (TIPS) or surgical porto-systemic shunts to control portal hypertension. The other two children, in whom the diagnosed was based on asymptomatic hepatomegaly, had normal renal function and structure with a more benign clinical course. Conclusions: The diagnosis of CHF should be suspected not only in children with polycystic kidney disease but in those children with persistent, hard consistency, left lobe predominance hepatomegaly.
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    Endovascular treatment of complex cerebral aneurysms with onyx hd-500 (R) in 38 patients
    (MASSON EDITEUR, 2011) Tevah, J.; Senf, R.; Cruz, J.; Fava, M.
    Objective. - To report our experience with Onyx HD-500 (R) (Micro Therapeutics, Inc., Irvine, CA, USA) in the endovascular treatment of complex intracranial aneurysms as an alternative to treatment with platinum coils.
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    Fibrosis Hepática congénita: un espectro clínico variable: Casos clínicos
    (2004) Harris, Paul R.; Fodor, D.; Cavagnaro, F.; Di Egidio, M.; Fava, M.
    Background: Congenital hepalic fibrosis (CHF) is an autosomic dominant disease that has been associated will polycistic kidney disease. Aim. To describe The medical managment of 5 children with CHF and to evaluate the presence and extension of the associated renal disease. Patients and methods. Retrospective review of the medical charts of 5 children with CHF aged 2 to 14 years. Results: Three children presented autosomic recessive polycistic kidney disease, which was diagnosed before the appearance of liver disease manifestations. They presented a more severe liver damage with a more aggressive clinical course requiring use of transjugular intrahepatic porto-systemic shunts (TIPS) or surgical porto-systemic shunts to control portal hypertension. The other two children, in whom the diagnosed was based on asymptomatic hepatomegaly had normal renal function and structure with a more benign clinical course. Conclusions: The diagnosis of CHT should be suspected not only in children with polycystic kidney disease but in those children with persistent, hard consistently, left lobe predominance hepatomegaly.
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    Using magnetic resonance phase-contrast velocity mapping for diagnosing pelvic congestion syndrome
    (ROYAL SOC MEDICINE PRESS LTD, 2011) Meneses, L. Q.; Uribe, S.; Tejos, C.; Andia, M. E.; Fava, M.; Irarrazaval, P.
    Objective: To evaluate phase-contrast velocity mapping (PCVM) as a diagnostic tool for pelvic congestion syndrome and comparing this approach with direct venography.